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KMID : 0357919800140040056
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Korean Journal of Pathology
1980 Volume.14 No. 4 p.56 ~ p.61
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Glanzmann's Thrombasthenia -Report of three patients
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안우성
박명희/조한익/김상인/양의조/최응상/김중곤/안효섭/홍창의
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Abstract
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Thrombasthenia is a rare disorder, apparently transmitted as an autosomal recessive
trait, in which platelet count is normal but bleeding time is greatly prolonged and clot
retraction is defective. The chief clinical finding is a tendency to develop purpura and
ecchymosis on trivial injury from early childhood but visceral hemorrhage and
hemarthroses are rare.
Epistaxes are common. The most striking feature, which is pathognomonic of this
disease, is a complete failure of the platelets to aggregate in response to any
concentration of ADP, epinephrine ana collagen.
The three cases, which meet the diagnostic criteria of Glanzmann's thrombasthenia, are
reported with review of the literatures.
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KEYWORD
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